CASE 1-2013: FATAL MANIFESTATION OF MYELOPROLIFERATIVE DISEASE

Case 1-2013: fatal manifestation of myeloproliferative disease.

Myeloproliferative disorders (MPDs) are defined as clonal stem cell diseases. the cardiovascular system is involved in 4 to 21% of MPD cases, presenting as acute ischemic coronary artery disease, valvular heart involvement, pericardial involvement, aortitis, thrombosis of major vessels, pulmonary embolism, systemic and pulmonary hypertension. Acute coronary syndrome may be the first manifestati...

Nekam’s Disease with Clinical Manifestation Simulating Darier's Disease: A Case Report

Nekam's disease is a rare dermatosis characterized by a distinctive seborrheic dermatitis with prominent facial eruption.  It is further associated with violaceous, papular, and/or nodular lesions on the extremities and trunk, typically arranged in a linear and reticulate pattern.  Herein, describe a patient with Nekam's disease, which resembled Darier’s disease in clinical manifestation.  The ...

A fatal case of Rosai–Dorfman disease

As Rosai-Dorfman Disease presents generally nonspecific symptoms, differential diagnosis can be of great learning curve for physicians. Additionally, RDD does not usually threaten life and spontaneous remission is frequently observed. However, unusually in our case the patient passed away within 1 month of confirmed diagnosis.

Hypoparathyroidism as a rare manifestation of Wilson,s disease: a case report

A 13 years old girl was admitted to the pediatric ward of hospital  No 1 of Kerman university of medical sciences because of crampy pains, pins and needles sensation of the extremities and history of an episode of seizure. Her problem started one week prior to admission with pain in the leg muscles, flexion of the fingers followed by seizure. On physical examination, the prominent finding inclu...

The Philadelphia chromosome in an unusual case of myeloproliferative disease.